Abstract
Introduction: Amyotrophic Lateral Sclerosis (ALS) is a degenerative disease that has a national reference center in Costa Rica. Based on the promulgation of Executive Decree 28838-H of July 17, 2000, the National Center for Pain Control and Palliative Care became the reference center for all patients with ALS, in order to improve quality of life of patients and families facing this disease. The objective of this study was to know the prevalence and other epidemiological variables of ALS in Costa Rica in the first semester of 2014. Methods: the data collection was made from the reports generated by the Integrated Health Information System. The database with the variables of sex, age and domicile of each patient was elaborated. Simple frequencies were performed and the prevalence was estimated for 2014, at the National Center for Pain Control and Palliative Care. Results: the population was 129 patients with an average age of 60 years. The gender distribution was 63% men and 37% women. A prevalence of 3.00 cases per 100,000 of the total population (95% CI, 2.48-3.52) was found. The study shows that the prevalence of patients with ALS is higher in the central valley. Conclusion: the prevalence of ALS in Costa Rica is within the expected worldwide, being more frequent in males.
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